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人 LAMP2/CD107b 基因ORF全长cDNA克隆(表达载体), C-Flag 标签

产品数据评论实验方法
表达宿主: Human Cells  
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13555-H08H-50
13555-H08H-200
50 µg 
200 µg 
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表达宿主: Human Cells  
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50791-M08H-50
50791-M08H-100
50 µg 
100 µg 
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表达宿主: Human Cells  
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90208-C08H-50
90208-C08H-100
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100 µg 
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反应性: Human  
应用 : WB  IHC-P  IF  IP  ICC/IF  
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13555-T46-50
13555-T46-200
13555-T46-100
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200 µg 
100 µg 
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反应性: Human  
应用 : 
    13555-RP01-400
    13555-RP01-200
    13555-RP01-100
    400 µg 
    200 µg 
    100 µg 
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    反应性: Mouse  
    应用 : ELISA  
      50791-RP01-400
      50791-RP01-200
      50791-RP01-100
      400 µg 
      200 µg 
      100 µg 
      Add to Cart
      反应性: Mouse  
      应用 : ELISA  
        50791-RP02-50
        50791-RP02-200
        50791-RP02-100
        50 µg 
        200 µg 
        100 µg 
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        反应性: Mouse  
        应用 : ELISA  
          50791-R102-50
          50791-R102-100
          50 µg 
          100 µg 
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          反应性: Mouse  
          应用 : ELISA  WB  
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          50791-T48-50
          50791-T48-200
          50791-T48-100
          50 µg 
          200 µg 
          100 µg 
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          LAMP2/CD107b cdna-clone 研究背景

          LAMP2 (Lysosomal-associated membrane protein 2), also known as CD107b (Cluster of Differentiation 107b), is a member of a family of membrane glycoproteins. This glycoprotein provides selectins with carbohydrate ligands. In human, LAMP2, the causative gene of Danon disease, located on chromosome Xq24, encodes the lysosome-associated membrane protein-2 (LAMP-2). LAMP-2 deficiency, or Danon disease, is a rare X-linked lysosomal disease characterized by cardiomyopathy, vacuolar myopathy, and mental retardation. LAMP2 cardiomyopathy is an X-linked and highly progressive myocardial storage disorder associated with diminished survival, which clinically resembles sarcomeric hypertrophic cardiomyopathy.

           LAMP2/CD107b cdna-clone 参考资料
        • Maron BJ, et al. (2010) Profound left ventricular remodeling associated with LAMP2 cardiomyopathy. Am J Cardiol. 106(8): 1194-6.
        • Di Blasi C, et al. (2008) Danon disease: a novel LAMP2 mutation affecting the pre-mRNA splicing and causing aberrant transcripts and partial protein expression. Neuromuscul Disord. 18(12): 962-6.
        • Echaniz-Laguna A, et al. (2006) Novel Lamp-2 gene mutation and successful treatment with heart transplantation in a large family with Danon disease. Muscle Nerve. 33(3): 393-7.
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